Int J Stomatol

Int J Stomatol ›› 2021, Vol. 48 ›› Issue (2): 213-217.doi: 10.7518/gjkq.2021027

• Reviews • Previous Articles     Next Articles

Oral and maxillofacial manifestations of Ehlers-Danlos syndrome

Liu Shuai1,2(),Wang Ningxiang1,3,Lin Liangyuan4,Wu Juan1()   

  1. 1. Dept. of Periodontology, Nanjing Stomatological Hospital, Medical School of Nanjing University, Nanjing 210008, China
    2. Dept. of Stomatology, Nanjing Lishui District Hospital of Traditional Chinese Medicine, Nanjing 211200, China
    3. Dept. of Stomatology, Nanjing Hospital of Chinese Medicine, Nanjing University of Traditional Chinese Medicine, Nanjing 210001, China
    4. Dept. of Stomatology, Children,s Hospital of Nanjing Medical University, Nanjing 210029, China
  • Received:2020-06-21 Revised:2020-10-31 Online:2021-03-01 Published:2021-03-17
  • Contact: Juan Wu E-mail:1729624217@qq.com;56868794@qq.com
  • Supported by:
    Medical Science and Technology Development Foundation, Nanjing Department of Health(YKK18121);Natural Science Foundation of Jiangsu Province(BK20200149)

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Abstract:

Ehlers-Danlos syndromes (EDS) belong to a clinically and genetically heterogeneous group of rare hereditary disorders characterised by varying degrees of connective tissue fragility, which affects the skin, ligaments, blood vessels and internal organs. Principal clinical features include tissue fragility, skin extensibility and joint hypermobility. Published data on the oral and maxillofacial manifestations of EDS are limited, but literature search found that almost all types of EDS have oral and maxillofacial changes, and these changes are often not correctly recognised by clinicians. This article reviews the oral and maxillofacial manifestations of EDS to provide reference for clinicians.

Key words: Ehlers-Danlos syndrome, oral, maxillofacial

CLC Number: 

  • R782.2

TrendMD: 
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