外胚叶发育不良综合征口腔临床诊疗的研究进展

doi:10.7518/gjkq.2022091

摘要/Abstract

摘要：

外胚叶发育不良综合征（EDs）是一类口腔先天性发育不良疾病的总称，表现为由外胚叶发育而来的多种组织包括毛发、指甲、牙齿、汗腺等发育不良。EDs常严重影响此类患者生长发育和身心健康。因此，对该类疾病进行早期诊断并及时治疗尤为重要。本文旨在对EDs口腔临床诊疗的研究进展作一综述，以期为口腔临床医生提供参考。

关键词: 外胚叶发育不良综合征, 临床分类, 疾病诊断, 治疗

Abstract:

Ectodermal dysplasia syndrome (EDs) is a general term of oral congenital dysplasia, and it is often characte-rized by dysplasia of various tissues developed from the ectodermal lobes, including hair, nails, teeth, and sweat glands. It often seriously affects the growth, development, physical, and mental health of these patients. Therefore, the early diagnosis and timely treatment of these diseases are particularly important. The purpose of this paper was to review the research progress of the clinical diagnosis and treatment of EDs to provide reference for oral clinicians.

Key words: ectodermal dysplasia syndrome, clinical classification, disease diagnosis, treatment

中图分类号:

R 44

朱星蓉,廖岚. 外胚叶发育不良综合征口腔临床诊疗的研究进展[J]. 国际口腔医学杂志, 2022, 49(6): 737-742.

Zhu Xingrong,Liao Lan. Research progress on oral clinical diagnosis and treatment of ectodermal dysplasia syndrome[J]. Int J Stomatol, 2022, 49(6): 737-742.

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